{"id":2180,"date":"2025-06-30T17:41:00","date_gmt":"2025-06-30T08:41:00","guid":{"rendered":"https:\/\/www.pharm.kyoto-u.ac.jp\/kuranaga-lab\/?post_type=paper&#038;p=2180"},"modified":"2026-07-23T17:53:33","modified_gmt":"2026-07-23T08:53:33","slug":"faseb-j-2025","status":"publish","type":"paper","link":"https:\/\/www.pharm.kyoto-u.ac.jp\/kuranaga-lab\/en\/paper\/faseb-j-2025\/","title":{"rendered":"Mitochondria-Homing Drug Mitochonic Acid 5 Improves Barth Syndrome Myopathy in a Human-Induced Pluripotent Stem Cell Model and Barth Syndrome Drosophila Model."},"content":{"rendered":"\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/40542649\/\" class=\"liinternal\">Mitochondria-Homing Drug Mitochonic Acid 5 Improves Barth Syndrome Myopathy in a Human-Induced Pluripotent Stem Cell Model and Barth Syndrome Drosophila Model.<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Tongu Y, Kasahara T, Matsuhashi T, Oikawa Y, Akimoto R, <strong>Luo Y<\/strong>, <strong>Sekine S<\/strong>, Suzuki M, Kashiwagi H, Kanno S, Tanaka Y, Sato K, Okubo Y, Muto A, Tokuno H, Suzuki C, Kawabe C, Ishikawa T, Watanabe S, Kikuchi K, Itai S, Sato T, Suzuki T, Igarashi K, Fukuda S, Soga T, Murayama K, <strong>Kuranaga E<\/strong>, Toyohara T, Abe T. <\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><strong><em>FASEB J.<\/em><\/strong> 2025 Jun 30;39(12):e70739. <\/p>\n\n\n\n<p class=\"wp-block-paragraph\">doi: 10.1096\/fj.202401856RRR.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tongu Y, et al.,  FASEB J. 2025 <\/p>\n","protected":false},"featured_media":0,"template":"","publication_category":[59],"publication_tag":[53],"class_list":["post-2180","paper","type-paper","status-publish","hentry","publication_category-publication","publication_tag-53"],"acf":[],"jetpack_sharing_enabled":true,"_links":{"self":[{"href":"https:\/\/www.pharm.kyoto-u.ac.jp\/kuranaga-lab\/en\/wp-json\/wp\/v2\/paper\/2180","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.pharm.kyoto-u.ac.jp\/kuranaga-lab\/en\/wp-json\/wp\/v2\/paper"}],"about":[{"href":"https:\/\/www.pharm.kyoto-u.ac.jp\/kuranaga-lab\/en\/wp-json\/wp\/v2\/types\/paper"}],"wp:attachment":[{"href":"https:\/\/www.pharm.kyoto-u.ac.jp\/kuranaga-lab\/en\/wp-json\/wp\/v2\/media?parent=2180"}],"wp:term":[{"taxonomy":"publication_category","embeddable":true,"href":"https:\/\/www.pharm.kyoto-u.ac.jp\/kuranaga-lab\/en\/wp-json\/wp\/v2\/publication_category?post=2180"},{"taxonomy":"publication_tag","embeddable":true,"href":"https:\/\/www.pharm.kyoto-u.ac.jp\/kuranaga-lab\/en\/wp-json\/wp\/v2\/publication_tag?post=2180"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}